{"id":157997,"date":"2026-07-17T09:36:36","date_gmt":"2026-07-17T09:36:36","guid":{"rendered":"https:\/\/pabau.com\/?p=157997"},"modified":"2026-08-17T11:49:49","modified_gmt":"2026-08-17T11:49:49","slug":"icd-10-code-m314","status":"publish","type":"post","link":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/","title":{"rendered":"ICD-10 Code M31.4: Aortic arch syndrome [Takayasu]"},"content":{"rendered":"\n<script type=\"application\/ld+json\">{\"@context\":\"https:\/\/schema.org\",\"@type\":\"MedicalWebPage\",\"headline\":\"ICD-10 Code M31.4: Aortic arch syndrome [Takayasu]\",\"description\":\"ICD-10 Code M31.4 (Aortic arch syndrome [Takayasu]) is a billable diagnosis code for Takayasu arteritis. Learn code details, synonyms, documentation requirements, and related codes.\",\"url\":\"https:\/\/pabau.com\/diagnostic-codes\/icd-10-code-m314\/\",\"audience\":{\"@type\":\"MedicalAudience\",\"audienceType\":\"Clinician\"},\"reviewedBy\":{\"@type\":\"Person\",\"name\":\"Dr Vanja Kitanova\",\"jobTitle\":\"Medical Reviewer\",\"affiliation\":{\"@type\":\"Organization\",\"name\":\"Pabau\"},\"knowsAbout\":[\"Medical Coding\",\"Clinical Documentation\",\"Healthcare Billing\",\"Clinical Safety\"],\"sameAs\":\"https:\/\/pabau.com\/blog\/author\/vanja\/\"},\"datePublished\":\"2026-07-17\",\"dateModified\":\"2026-07-17\"}<\/script>\n\n\n        <div id=\"key_takeaways\">\n            <div class=\"header\">\n                                    <img decoding=\"async\" src=\"https:\/\/pabau.com\/wp-content\/uploads\/2025\/12\/Key-Takeaways-Icon.svg\" alt=\"Key Takeaways\" height=\"42\" width=\"42\">\n                                <h3>Key Takeaways<\/h3>\n            <\/div>\n            <div class=\"list\">\n                                                            <div class=\"item\">\n                            <div>\n                                <svg width=\"20\" height=\"27\" viewBox=\"0 0 20 27\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\">\n                                    <path\n                                        d=\"M18.6223 14.3857C19.1246 13.8975 19.1246 13.1045 18.6223 12.6162L12.1938 6.36621C11.6915 5.87793 10.8759 5.87793 10.3737 6.36621C9.87143 6.85449 9.87143 7.64746 10.3737 8.13574L14.6125 12.2529H2.28571C1.57455 12.2529 1 12.8115 1 13.5029C1 14.1943 1.57455 14.7529 2.28571 14.7529H14.6085L10.3777 18.8701C9.87545 19.3584 9.87545 20.1514 10.3777 20.6396C10.8799 21.1279 11.6955 21.1279 12.1978 20.6396L18.6263 14.3896L18.6223 14.3857Z\"\n                                        fill=\"#3D3D46\" \/>\n                                <\/svg>\n                            <\/div>\n                            <p>ICD-10 Code M31.4 is the billable diagnosis code for aortic arch syndrome [Takayasu], effective October 1, 2025 for the 2026 ICD-10-CM edition.<\/p>\n                        <\/div>\n                                                                                <div class=\"item\">\n                            <div>\n                                <svg width=\"20\" height=\"27\" viewBox=\"0 0 20 27\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\">\n                                    <path\n                                        d=\"M18.6223 14.3857C19.1246 13.8975 19.1246 13.1045 18.6223 12.6162L12.1938 6.36621C11.6915 5.87793 10.8759 5.87793 10.3737 6.36621C9.87143 6.85449 9.87143 7.64746 10.3737 8.13574L14.6125 12.2529H2.28571C1.57455 12.2529 1 12.8115 1 13.5029C1 14.1943 1.57455 14.7529 2.28571 14.7529H14.6085L10.3777 18.8701C9.87545 19.3584 9.87545 20.1514 10.3777 20.6396C10.8799 21.1279 11.6955 21.1279 12.1978 20.6396L18.6263 14.3896L18.6223 14.3857Z\"\n                                        fill=\"#3D3D46\" \/>\n                                <\/svg>\n                            <\/div>\n                            <p>The code captures Takayasu arteritis, a rare large-vessel granulomatous vasculitis affecting the aorta and its main branches, also called pulseless disease.<\/p>\n                        <\/div>\n                                                                                <div class=\"item\">\n                            <div>\n                                <svg width=\"20\" height=\"27\" viewBox=\"0 0 20 27\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\">\n                                    <path\n                                        d=\"M18.6223 14.3857C19.1246 13.8975 19.1246 13.1045 18.6223 12.6162L12.1938 6.36621C11.6915 5.87793 10.8759 5.87793 10.3737 6.36621C9.87143 6.85449 9.87143 7.64746 10.3737 8.13574L14.6125 12.2529H2.28571C1.57455 12.2529 1 12.8115 1 13.5029C1 14.1943 1.57455 14.7529 2.28571 14.7529H14.6085L10.3777 18.8701C9.87545 19.3584 9.87545 20.1514 10.3777 20.6396C10.8799 21.1279 11.6955 21.1279 12.1978 20.6396L18.6263 14.3896L18.6223 14.3857Z\"\n                                        fill=\"#3D3D46\" \/>\n                                <\/svg>\n                            <\/div>\n                            <p>Accurate use of ICD-10 Code M31.4 requires documented specialist confirmation, vessel involvement, and disease activity in the medical record.<\/p>\n                        <\/div>\n                                                                                <div class=\"item\">\n                            <div>\n                                <svg width=\"20\" height=\"27\" viewBox=\"0 0 20 27\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\">\n                                    <path\n                                        d=\"M18.6223 14.3857C19.1246 13.8975 19.1246 13.1045 18.6223 12.6162L12.1938 6.36621C11.6915 5.87793 10.8759 5.87793 10.3737 6.36621C9.87143 6.85449 9.87143 7.64746 10.3737 8.13574L14.6125 12.2529H2.28571C1.57455 12.2529 1 12.8115 1 13.5029C1 14.1943 1.57455 14.7529 2.28571 14.7529H14.6085L10.3777 18.8701C9.87545 19.3584 9.87545 20.1514 10.3777 20.6396C10.8799 21.1279 11.6955 21.1279 12.1978 20.6396L18.6263 14.3896L18.6223 14.3857Z\"\n                                        fill=\"#3D3D46\" \/>\n                                <\/svg>\n                            <\/div>\n                            <p>Pabau&#8217;s claims management software helps rheumatology and vascular practices attach the correct ICD-10 diagnosis codes to procedures and reduce claim errors.<\/p>\n                        <\/div>\n                                                <\/div>\n        <\/div>\n    \n\n\n<p class=\"wp-block-paragraph\">ICD-10 Code M31.4 is the billable diagnosis code for aortic arch syndrome [Takayasu], the ICD-10-CM label for Takayasu arteritis. It covers confirmed cases of this large-vessel granulomatous vasculitis affecting the aorta and its main branches, effective October 1, 2025 for the 2026 ICD-10-CM edition.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">This reference covers ICD-10 Code M31.4 in full: its billable status, the clinical picture that justifies its use, synonyms accepted by the ICD-10-CM index, the code hierarchy, related vasculitis codes, documentation requirements, associated CPT codes, and the ICD-9-CM crosswalk.<\/p>\n\n\n\n<figure class=\"wp-block-embed is-type-video is-provider-youtube wp-block-embed-youtube wp-embed-aspect-16-9 wp-has-aspect-ratio\"><div class=\"wp-block-embed__wrapper\">\n<iframe title=\"ICD-10 Revisions: Stay Updated or Fall Behind\" width=\"800\" height=\"450\" src=\"https:\/\/www.youtube.com\/embed\/bqAyb-BCA0w?feature=oembed\" frameborder=\"0\" allow=\"accelerometer; autoplay; clipboard-write; encrypted-media; gyroscope; picture-in-picture; web-share\" referrerpolicy=\"strict-origin-when-cross-origin\" allowfullscreen><\/iframe>\n<\/div><\/figure>\n\n\n\n<h2 id=\"h-icd-10-code-m31-4-code-details-and-billable-status\" class=\"wp-block-heading\">ICD-10 Code M31.4: Code details and billable status<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">ICD-10 Code M31.4 is a billable and specific ICD-10-CM diagnosis code. No additional characters are required to make it valid for claim submission. The table below captures the core code facts that coders and billers need at a glance.<\/p>\n\n\n\n<table style=\"width:100%;border-collapse:separate;border-spacing:0;border-radius:12px;overflow:hidden;font-size:15px;line-height:1.5;margin:1.5em 0 2em;box-shadow:0 2px 12px rgba(0,0,0,0.08)\">\n<thead>\n<tr>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">Field<\/th>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">Value<\/th>\n<\/tr>\n<\/thead>\n<tbody>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">Code<\/td>\n<td style=\"padding:12px 16px;color:#374151\">M31.4<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0;background:#F9FAFB\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">Full description<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Aortic arch syndrome [Takayasu]<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">Code type<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Diagnosis (ICD-10-CM)<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0;background:#F9FAFB\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">Billable \/ specific<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Yes. No further specificity required.<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">ICD-10-CM edition<\/td>\n<td style=\"padding:12px 16px;color:#374151\">2026 (effective October 1, 2025)<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0;background:#F9FAFB\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">Classification block<\/td>\n<td style=\"padding:12px 16px;color:#374151\">M30-M36: Systemic connective tissue disorders<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">Parent category<\/td>\n<td style=\"padding:12px 16px;color:#374151\">M31: Other necrotizing vasculopathies<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0;background:#F9FAFB\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">Applicable to<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Takayasu&#8217;s arteritis; Takayasu disease; pulseless disease<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n\n\n\n<p class=\"wp-block-paragraph\">According to the <a href=\"https:\/\/icd10cmtool.cdc.gov\/\" target=\"_blank\" rel=\"nofollow noopener\">CDC\/NCHS ICD-10-CM web tool<\/a>, M31.4 has been a valid, billable code since its adoption under ICD-10-CM and remains active in the 2026 edition. Coders working with claims management software can confirm this status directly within their billing workflow rather than relying on printed code books.<\/p>\n\n\n\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/cdn.pabau.com\/cdn\/attachments\/pulse\/content-engine\/diagnostic_codes\/icd-10-code-m314\/automate-claims-through-healthcode.webp\" alt=\"Automate claims and billing with Pabau\"\/><figcaption class=\"wp-element-caption\"><em>Automate claims and billing with Pabau<\/em><\/figcaption><\/figure>\n\n\n\n<div style=\"height:20px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<h2 id=\"h-what-is-aortic-arch-syndrome-takayasu-arteritis\" class=\"wp-block-heading\">What is aortic arch syndrome (Takayasu arteritis)?<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">Takayasu arteritis is a rare, chronic, granulomatous large-vessel vasculitis. It targets the aorta and its primary branches, causing transmural inflammation that leads to stenosis, occlusion, or aneurysm formation over time.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">The condition primarily affects women of childbearing age, with peak incidence between 15 and 40 years. It occurs worldwide but is more prevalent in East Asian and South Asian populations, according to peer-reviewed epidemiological literature.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">From a coding standpoint, the name &#8220;aortic arch syndrome&#8221; reflects the anatomical territory most commonly involved: the aortic arch and its branches, including the subclavian, carotid, and renal arteries. The histopathological hallmark is granulomatous inflammation with giant cells, which places it alongside giant cell arteritis (M31.5) in the same parent category.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">The key clinical distinction is age of onset: Takayasu affects patients under 40; giant cell arteritis typically presents over 50.<\/p>\n\n\n\n<h2 id=\"h-synonyms-and-alternate-names-accepted-under-m31-4\" class=\"wp-block-heading\">Synonyms and alternate names accepted under M31.4<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">The ICD-10-CM index accepts several terms that all map to ICD-10 Code M31.4. Using any of these in clinical documentation is acceptable, provided the diagnosis is confirmed and the documentation meets specificity requirements.<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Aortic arch syndrome [Takayasu]<\/strong> &#8211; the official ICD-10-CM descriptor<\/li>\n\n\n\n<li><strong>Takayasu arteritis<\/strong> &#8211; the most common rheumatology and vascular surgery term<\/li>\n\n\n\n<li><strong>Takayasu&#8217;s arteritis<\/strong> &#8211; possessive form, equally accepted<\/li>\n\n\n\n<li><strong>Takayasu disease<\/strong> &#8211; alternate disease-name form<\/li>\n\n\n\n<li><strong>Pulseless disease<\/strong> &#8211; historical name derived from the loss of radial pulse in advanced disease<\/li>\n\n\n\n<li><strong>Aortoarteritis<\/strong> &#8211; a descriptor used in some international and South Asian literature<\/li>\n<\/ul>\n\n\n\n<p class=\"wp-block-paragraph\">When the medical record uses any of these terms, the coder can confidently assign M31.4 without querying the provider. If the documentation says &#8220;probable Takayasu&#8221; or &#8220;suspected aortoarteritis,&#8221; do not code M31.4 yet. ICD-10-CM Official Guidelines require confirmed diagnoses for outpatient encounters.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">For inpatient encounters, conditions described as &#8220;probable&#8221; may be coded as confirmed. Even then, a rheumatologist or vascular specialist&#8217;s attestation strengthens the record. Practices using structured clinical records can flag these nuances in the patient chart before the claim is submitted.<\/p>\n\n\n\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/cdn.pabau.com\/cdn\/attachments\/pulse\/content-engine\/diagnostic_codes\/icd-10-code-m314\/comprehensive-patient-records.webp\" alt=\"Comprehensive patient records\"\/><figcaption class=\"wp-element-caption\"><em>Comprehensive patient records<\/em><\/figcaption><\/figure>\n\n\n\n<div style=\"height:20px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n\n<h2 id=\"h-m31-4-in-the-icd-10-cm-code-hierarchy\" class=\"wp-block-heading\">M31.4 in the ICD-10-CM code hierarchy<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">Understanding where ICD-10 Code M31.4 sits within the ICD-10-CM tabular list helps coders select the right code when multiple vasculitis codes are under consideration. The hierarchy flows from broad to specific.<\/p>\n\n\n\n<table style=\"width:100%;border-collapse:separate;border-spacing:0;border-radius:12px;overflow:hidden;font-size:15px;line-height:1.5;margin:1.5em 0 2em;box-shadow:0 2px 12px rgba(0,0,0,0.08)\">\n<thead>\n<tr>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">Level<\/th>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">Code \/ Block<\/th>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">Description<\/th>\n<\/tr>\n<\/thead>\n<tbody>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">Chapter<\/td>\n<td style=\"padding:12px 16px;color:#374151\">M00-M99<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Diseases of the musculoskeletal system and connective tissue<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0;background:#F9FAFB\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">Block<\/td>\n<td style=\"padding:12px 16px;color:#374151\">M30-M36<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Systemic connective tissue disorders<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">Category<\/td>\n<td style=\"padding:12px 16px;color:#374151\">M31<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Other necrotizing vasculopathies<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0;background:#F9FAFB\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">Code<\/td>\n<td style=\"padding:12px 16px;color:#374151\">M31.4<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Aortic arch syndrome [Takayasu] &#8211; billable, specific<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n\n\n\n<p class=\"wp-block-paragraph\">The sibling codes within M31 are clinically distinct, and coders should not treat this category as interchangeable. The <a href=\"https:\/\/www.cms.gov\/medicare\/coding-billing\/icd-10-codes\" target=\"_blank\" rel=\"nofollow noopener\">CMS ICD-10 codes page<\/a> provides the official tabular list and annual update files for the full M31 group.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Key siblings relevant to vasculitis coding include M31.0 (hypersensitivity angiitis), M31.1 (thrombotic microangiopathy), M31.30\/M31.31 (Wegener&#8217;s granulomatosis, coded to a 5th character), M31.5 (giant cell arteritis with polymyalgia rheumatica), and M31.6 (other giant cell arteritis).<\/p>\n\n\n\n<h2 id=\"h-related-icd-10-codes-for-vasculitis-and-arteritis\" class=\"wp-block-heading\">Related ICD-10 codes for vasculitis and arteritis<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">Differentiating ICD-10 Code M31.4 from adjacent vasculitis codes is one of the most common coding challenges in rheumatology. The table below covers the codes most likely to appear on the same differential as Takayasu arteritis.<\/p>\n\n\n\n<table style=\"width:100%;border-collapse:separate;border-spacing:0;border-radius:12px;overflow:hidden;font-size:15px;line-height:1.5;margin:1.5em 0 2em;box-shadow:0 2px 12px rgba(0,0,0,0.08)\">\n<thead>\n<tr>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">Code<\/th>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">Description<\/th>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">Key distinction from M31.4<\/th>\n<\/tr>\n<\/thead>\n<tbody>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">M31.4<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Aortic arch syndrome [Takayasu]<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Large-vessel; onset under 40; aorta and main branches<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0;background:#F9FAFB\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">M31.5<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Giant cell arteritis with polymyalgia rheumatica<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Large-vessel; onset over 50; cranial artery tropism; PMR co-occurs<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">M31.6<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Other giant cell arteritis<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Large-vessel; onset over 50; no PMR component<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0;background:#F9FAFB\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">M30.0<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Polyarteritis nodosa<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Medium-vessel; necrotizing; no granulomata<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">M31.30<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Wegener&#8217;s granulomatosis without renal involvement<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Small-vessel; ANCA-associated; upper\/lower respiratory involvement. Parent code M31.3 is non-billable; a 5th character is required.<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0;background:#F9FAFB\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">M31.31<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Wegener&#8217;s granulomatosis with renal involvement<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Small-vessel; ANCA-associated; upper\/lower respiratory and renal involvement<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">I77.6<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Arteritis, unspecified<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Use only when type of arteritis is not documented; avoid when Takayasu is confirmed<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n\n\n\n<p class=\"wp-block-paragraph\">The AAPC&#8217;s <a href=\"https:\/\/www.aapc.com\/codes\/icd-10-codes-range\/\" target=\"_blank\" rel=\"nofollow noopener\">ICD-10-CM code search<\/a> provides full inclusion notes and exclusion markers for each of these codes. Coders researching the M31 group should check that tool alongside the official tabular list. For practices managing rheumatology billing.<\/p>\n\n\n\n<h2 id=\"h-clinical-documentation-requirements-for-icd-10-code-m31-4\" class=\"wp-block-heading\">Clinical documentation requirements for ICD-10 Code M31.4<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">A claim submitted with M31.4 will face scrutiny if the medical record does not support the diagnosis. Payers and auditors look for specific documentation elements. Missing any one of them is enough to trigger a request for additional information or a denial.<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Confirmed diagnosis statement:<\/strong> The record must include a clear statement that the diagnosing clinician confirms Takayasu arteritis. &#8220;Suspected&#8221; or &#8220;possible&#8221; language does not support M31.4 in outpatient coding.<\/li>\n\n\n\n<li><strong>Specialist attestation:<\/strong> A rheumatologist or vascular surgeon&#8217;s confirmation strengthens the claim. Primary care documentation alone, without specialist referral notes, may not survive audit.<\/li>\n\n\n\n<li><strong>Vessel involvement:<\/strong> Document which vessels are affected. Subclavian stenosis, carotid occlusion, or aortic wall thickening should be named explicitly rather than described as &#8220;vascular disease.&#8221;<\/li>\n\n\n\n<li><strong>Disease activity status:<\/strong> Coders and auditors expect notes to reflect whether the patient is in an active inflammatory phase or remission. This context matters for associated CPT code selection (see below).<\/li>\n\n\n\n<li><strong>Imaging or angiographic evidence:<\/strong> CT angiography, MRI angiography, or PET scan findings that demonstrate large-vessel inflammation or stenosis should be referenced in the clinical note, not just filed separately as a radiology report.<\/li>\n<\/ul>\n\n\n\n<p class=\"wp-block-paragraph\">Practices using digital intake forms can build structured templates that prompt clinicians to capture these data points at the point of care, reducing the need for addenda requests later.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Specificity in the clinical note is what converts a billable code into a paid claim. Without it.<\/p>\n\n\n\n<figure class=\"wp-block-image size-large\"><img decoding=\"async\" src=\"https:\/\/cdn.pabau.com\/cdn\/attachments\/pulse\/content-engine\/diagnostic_codes\/icd-10-code-m314\/how-to-mark-injection-points-in-a-treatment-note.webp\" alt=\"How to Mark Injection Points in a Treatment Note\"\/><figcaption class=\"wp-element-caption\"><em>How to Mark Injection Points in a Treatment Note<\/em><\/figcaption><\/figure>\n\n\n\n<div style=\"height:20px\" aria-hidden=\"true\" class=\"wp-block-spacer\"><\/div>\n\n\n        <div id=\"pro_tip\">\n            <div class=\"img\">\n                <svg width=\"42\" height=\"42\" viewBox=\"0 0 42 42\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\">\n                    <path fill-rule=\"evenodd\" clip-rule=\"evenodd\"\n                        d=\"M12.6383 19.5238C12.6632 21.2071 12.8734 22.9926 12.0685 24.5523C11.0341 26.8917 8.45076 28.169 7.56292 30.5918C6.63082 33.1061 7.19505 36.185 9.31371 37.9786C10.929 39.5678 13.4183 39.9873 15.6061 39.5463C17.4592 39.073 19.1049 37.8388 19.9706 36.1608C20.781 34.7141 20.7866 32.9904 20.5293 31.3985C20.1006 29.3092 18.3775 27.8705 16.9807 26.362C14.8814 24.1005 14.6684 20.6854 15.595 17.8915C16.4331 15.4768 19.0026 14.2344 20.0425 11.9461C20.7202 10.6769 20.7506 9.20327 20.6068 7.81304C20.1864 5.40098 18.3139 3.23631 15.8716 2.56674C13.9742 2.03969 11.8224 2.30052 10.1739 3.37614C8.70522 4.34688 7.5878 5.86618 7.28356 7.58178C6.76081 9.82981 7.53525 12.2822 9.20307 13.9118C10.7658 15.4741 12.4806 17.2273 12.6383 19.5238Z\"\n                        fill=\"#2BADD4\" \/>\n                    <path fill-rule=\"evenodd\" clip-rule=\"evenodd\"\n                        d=\"M22.7048 19.8387C22.6822 22.3279 24.4507 24.6234 26.7493 25.4682C28.0531 25.961 29.4725 25.9183 30.7989 25.5487C32.0575 24.9955 33.301 24.2237 34.0069 23.0092C34.8384 21.5811 35.2982 19.8286 34.7832 18.2094C34.3611 16.2507 32.8739 14.6541 31.0275 13.9426C28.6736 12.9595 25.8073 13.7942 24.1719 15.7001C23.2022 16.8366 22.6143 18.3326 22.7048 19.8387Z\"\n                        fill=\"#2BADD4\" \/>\n                <\/svg>\n            <\/div>\n            <div class=\"text\">\n                <h3>Pro Tip<\/h3>\n                <p>Document the ACR\/EULAR classification criteria your rheumatologist used to confirm Takayasu arteritis. Naming the specific criteria (such as age of disease onset under 40, or arteriographic evidence of aortic or subclavian narrowing) directly in the clinical note gives auditors a clear, defensible basis for M31.4 and virtually eliminates provider query requests on this code.<\/p>\n            <\/div>\n        <\/div>\n    \n\n\n<h2 id=\"h-symptoms-and-diagnostic-criteria-relevant-to-coding\" class=\"wp-block-heading\">Symptoms and diagnostic criteria relevant to coding<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">Coders do not diagnose. But understanding the clinical picture helps verify that the documentation supports M31.4 before submission, and it informs the selection of associated procedure codes. The ACR classification criteria for Takayasu arteritis require at least three of six criteria to be met for classification. The criteria most frequently referenced in coding-relevant documentation include:<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li>Age of disease onset at or under 40 years<\/li>\n\n\n\n<li>Claudication of an extremity (limb fatigue or discomfort with activity)<\/li>\n\n\n\n<li>Decreased brachial artery pulse on at least one side<\/li>\n\n\n\n<li>Blood pressure difference greater than 10 mmHg between arms<\/li>\n\n\n\n<li>Bruit over a subclavian artery or the aorta on auscultation<\/li>\n\n\n\n<li>Arteriographic evidence of narrowing or occlusion of the aorta, its primary branches, or large arteries in the proximal upper or lower extremities<\/li>\n<\/ul>\n\n\n\n<p class=\"wp-block-paragraph\">The sixth criterion, the angiographic finding, is the one most commonly recorded in imaging reports rather than the clinical note itself. Coders should confirm the treating physician has referenced this finding in their note, not just in a separate radiology report, to establish the link between the imaging and the confirmed diagnosis.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Practices managing complex rheumatology cases benefit from keeping imaging references and clinical impressions in one accessible patient record.<\/p>\n\n\n\n<h2 id=\"h-associated-cpt-codes-for-m31-4-procedures\" class=\"wp-block-heading\">Associated CPT codes for M31.4 procedures<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">M31.4 as a diagnosis code pairs with a range of CPT procedure codes depending on the clinical encounter type. The table below covers the CPT codes most commonly associated with Takayasu arteritis management. Verify each against the current AMA CPT code set before submission, as code descriptors and coverage policies are subject to annual updates.<\/p>\n\n\n\n<table style=\"width:100%;border-collapse:separate;border-spacing:0;border-radius:12px;overflow:hidden;font-size:15px;line-height:1.5;margin:1.5em 0 2em;box-shadow:0 2px 12px rgba(0,0,0,0.08)\">\n<thead>\n<tr>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">CPT Code<\/th>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">Description<\/th>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">Clinical context<\/th>\n<\/tr>\n<\/thead>\n<tbody>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">99213-99215<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Office or outpatient visit, established patient<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Rheumatology follow-up, disease activity monitoring<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0;background:#F9FAFB\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">93922<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Limited bilateral noninvasive physiologic studies of upper or lower extremity arteries<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Pulse volume recording, ankle-brachial index for vascular monitoring<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">75600<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Aortography, thoracic, without serialography, radiological supervision and interpretation<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Aortic arch imaging for initial diagnosis or disease progression assessment<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0;background:#F9FAFB\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">96413<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Chemotherapy administration, intravenous infusion technique, up to 1 hour<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Biologic or immunosuppressive infusion (e.g. tocilizumab) for active Takayasu<\/td>\n<\/tr>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">71275<\/td>\n<td style=\"padding:12px 16px;color:#374151\">CT angiography, chest (non-coronary), with contrast, including 3D rendering<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Chest CTA for aortic arch and great vessel stenosis mapping and follow-up imaging<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n\n\n\n<p class=\"wp-block-paragraph\">The CPT codes above are indicative based on typical Takayasu arteritis clinical pathways. Confirm medical necessity linkage to M31.4 for each code individually, and verify payer-specific LCD\/NCD policies before submitting.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Practices often pair 99214 follow-up visits with 96413 infusion codes when biologic therapy is active. Integrated claims management software that flags common M31.4-CPT combinations catches mismatches before a claim leaves the practice.<\/p>\n\n\n        <div id=\"book_a_demo\">\n            <div class=\"left-side\">\n                <div class=\"logo\">\n                    <img decoding=\"async\"\n                        src=\"https:\/\/pabau.com\/wp-content\/uploads\/2026\/01\/Logo.svg\"\n                        alt=\"Logo\"\n                        loading=\"lazy\"\n                    \/>\n                <\/div>\n\n                <h3 class=\"heading\">\n                    Streamline your ICD-10 billing workflows                <\/h3>\n\n                <p class=\"description\">\n                    Pabau helps rheumatology and vascular practices attach accurate ICD-10 diagnosis codes to procedures, automate documentation prompts, and reduce claim errors. See how it works for your specialty.                <\/p>\n\n                <div class=\"button-group\">\n                    <a href=\"\/book-demo\/\" class=\"btn btn-scale-effect btn-cta-color btn-md\">\n                        <span class=\"btn-text\">Book a demo<\/span>\n                        <div class=\"btn-icon btn-icon-right\" aria-hidden=\"true\">\n                            <svg\n                                width=\"14\"\n                                height=\"12\"\n                                viewBox=\"0 0 14 12\"\n                                fill=\"none\"\n                                xmlns=\"http:\/\/www.w3.org\/2000\/svg\"\n                            >\n                                <path\n                                    d=\"M0.75 4.77295C0.335786 4.77295 0 5.10874 0 5.52295C0 5.93716 0.335786 6.27295 0.75 6.27295V5.52295V4.77295ZM13.2803 6.05328C13.5732 5.76039 13.5732 5.28551 13.2803 4.99262L8.50736 0.219648C8.21447 -0.073245 7.73959 -0.073245 7.4467 0.219648C7.15381 0.512542 7.15381 0.987415 7.4467 1.28031L11.6893 5.52295L7.4467 9.76559C7.15381 10.0585 7.15381 10.5334 7.4467 10.8263C7.73959 11.1191 8.21447 11.1191 8.50736 10.8263L13.2803 6.05328ZM0.75 5.52295V6.27295L12.75 6.27295V5.52295V4.77295L0.75 4.77295V5.52295Z\"\n                                    fill=\"currentColor\"\n                                ><\/path>\n                            <\/svg>\n                        <\/div>\n                    <\/a>\n                <\/div>\n            <\/div>\n\n            <div class=\"right-side\">\n                <img decoding=\"async\"\n                    src=\"https:\/\/pabau.com\/wp-content\/uploads\/2026\/01\/Home-Page-Concept-4.webp\"\n                    alt=\"Pabau practice management software for ICD-10 billing workflows\"\n                    loading=\"lazy\"\n                \/>\n            <\/div>\n        <\/div>\n        \n\n\n<h2 id=\"h-icd-9-cm-to-icd-10-code-m31-4-crosswalk\" class=\"wp-block-heading\">ICD-9-CM to ICD-10 Code M31.4 crosswalk<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">Legacy system transitions, retrospective audits, and some payer reporting requirements still involve ICD-9-CM codes. The General Equivalence Mappings (GEMs) maintained by CMS and CDC\/NCHS provide the official crosswalk. According to the <a href=\"https:\/\/resdac.org\/articles\/international-classification-disease-icd-codes-medicare-files\" target=\"_blank\" rel=\"nofollow noopener\">ResDAC ICD coding resources<\/a>, coders should always cite the official GEMs file when documenting crosswalk rationale for audit purposes, rather than relying on third-party conversion tools alone.<\/p>\n\n\n\n<table style=\"width:100%;border-collapse:separate;border-spacing:0;border-radius:12px;overflow:hidden;font-size:15px;line-height:1.5;margin:1.5em 0 2em;box-shadow:0 2px 12px rgba(0,0,0,0.08)\">\n<thead>\n<tr>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">ICD-9-CM Code<\/th>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">ICD-9-CM Description<\/th>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">ICD-10-CM Code<\/th>\n<th style=\"background:#121D36;color:#fff;padding:14px 16px;text-align:left;font-weight:600;font-size:14px;letter-spacing:0.3px;border-bottom:2px solid #2BADD4\">Mapping type<\/th>\n<\/tr>\n<\/thead>\n<tbody>\n<tr style=\"border-bottom:1px solid #E8ECF0\">\n<td style=\"padding:12px 16px;font-weight:600;color:#121D36\">446.7<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Takayasu&#8217;s disease<\/td>\n<td style=\"padding:12px 16px;color:#374151\">M31.4<\/td>\n<td style=\"padding:12px 16px;color:#374151\">Approximate (forward, one-to-one)<\/td>\n<\/tr>\n<\/tbody>\n<\/table>\n\n\n\n<p class=\"wp-block-paragraph\">ICD-9-CM code 446.7 (Takayasu&#8217;s disease) maps forward to M31.4 as an approximate equivalent. The mapping is one-to-one, making this a relatively clean crosswalk compared to some conditions where ICD-9 codes fan out to multiple ICD-10 options.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Coders handling retroactive audits or payer reconciliation should confirm this against the current GEMs file. Practices pairing crosswalk tables with their EHR&#8217;s code search get faster retrospective lookups when the same reference feeds both systems.<\/p>\n\n\n\n<h2 id=\"h-coding-tips-and-common-errors-with-icd-10-code-m31-4\" class=\"wp-block-heading\">Coding tips and common errors with ICD-10 Code M31.4<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">Three patterns account for most M31.4 errors seen in rheumatology and vascular coding audits. Each is preventable with the right review process.<\/p>\n\n\n\n<ul class=\"wp-block-list\">\n<li><strong>Confusing M31.4 with the giant cell arteritis codes M31.5 or <a href=\"https:\/\/pabau.com\/diagnostic-codes\/icd-10-code-m316\/\">M31.6<\/a>:<\/strong> Both are large-vessel granulomatous vasculitides. The clinical separator is age of onset. If the record says the patient is 62 with jaw claudication and scalp tenderness, M31.5 or M31.6 is the correct code, not M31.4. Always confirm the patient&#8217;s age and the affected vessel territory before finalizing the code.<\/li>\n\n\n\n<li><strong>Coding from the presenting symptom rather than the confirmed diagnosis:<\/strong> Presenting complaints like arm claudication, pulse asymmetry, or hypertension that is hard to control are symptoms, not diagnoses. Assign M31.4 only when the physician&#8217;s note confirms the Takayasu arteritis diagnosis. If the visit is for a symptom during the diagnostic workup, code the symptom.<\/li>\n\n\n\n<li><strong>Omitting additional codes for complications or comorbidities:<\/strong> Active Takayasu arteritis frequently co-occurs with I10 hypertension, renal artery stenosis (I70.1), or aortic aneurysm (I71-range codes). These should be coded as additional diagnoses when documented, not absorbed into M31.4. Failing to code them leaves revenue on the table and understates clinical complexity for HCC risk adjustment purposes.<\/li>\n<\/ul>\n\n\n\n<p class=\"wp-block-paragraph\">Practices building coding workflows in a practice management platform can set up code pairing alerts that prompt coders to check for these common co-occurring conditions when M31.4 is selected. The <a href=\"https:\/\/www.icd10data.com\/\" target=\"_blank\" rel=\"nofollow noopener\">ICD10Data.com lookup tool<\/a> is also useful for quickly verifying code inclusions and exclusions during chart review.<\/p>\n\n\n\n<h2 class=\"wp-block-heading\">Related ICD-10 codes<\/h2>\n\n\n\n<ul class=\"wp-block-list\">\n<li><a href=\"https:\/\/pabau.com\/diagnostic-codes\/icd-10-code-m1990\/\">ICD-10 code M19.90 \u2014 Degenerative Joint Disease Documentation<\/a><\/li>\n\n\n<li><a href=\"https:\/\/pabau.com\/diagnostic-codes\/icd-10-code-m315\/\">ICD-10 code M31.5 \u2014 Giant cell arteritis with polymyalgia rheumatica<\/a><\/li>\n\n\n<li><a href=\"https:\/\/pabau.com\/diagnostic-codes\/icd-10-code-m317\/\">ICD-10 code M31.7 \u2014 Microscopic polyangiitis<\/a><\/li>\n<\/ul>\n\n\n\n<h2 id=\"h-how-pabau-supports-icd-10-coding-workflows\" class=\"wp-block-heading\">How Pabau supports ICD-10 coding workflows<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">Rare codes like ICD-10 Code M31.4 expose weaknesses in manual coding processes. When a rheumatologist sees one Takayasu case every few months, the documentation prompts are not embedded in anyone&#8217;s memory. They need to be embedded in the clinical workflow instead.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Pabau&#8217;s structured patient records let practices build specialty-specific note templates that prompt for the documentation elements M31.4 requires: confirmed diagnosis language, specialist attestation, vessel involvement, disease activity status, and imaging references. These prompts reduce addenda requests, cut the time between encounter and claim submission, and make the record audit-ready from the moment the clinician closes the note.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">The platform&#8217;s claims management features allow practices to create code pairing rules, flag common M31.4-CPT combinations, and track denial patterns by code. For rheumatology and vascular practices handling complex, rare diagnoses, that kind of code-level intelligence is what separates a clean claim from a rework cycle.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">More context on how HIPAA-compliant practice software supports documentation integrity is available in our compliance guide.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Practices wanting a broader view of specialty workflows can see how Pabau adapts across primary care and <a href=\"https:\/\/pabau.com\/industry\/physical-therapy-emr\/\">physical therapy<\/a> practices alike.<\/p>\n\n\n\n<h2 id=\"h-conclusion\" class=\"wp-block-heading\">Conclusion<\/h2>\n\n\n\n<p class=\"wp-block-paragraph\">ICD-10 Code M31.4 is straightforward to identify but easy to misassign. The most common errors, confusing it with M31.5, coding before diagnosis confirmation, and missing co-occurring conditions, are each addressable through better documentation prompts and code review workflows.<\/p>\n\n\n\n<p class=\"wp-block-paragraph\">Pabau&#8217;s structured clinical records and claims management tools give rheumatology and vascular practices the workflow scaffolding they need to code rare diagnoses accurately from the first submission. See how leading EMR platforms handle rare code documentation, or speak with the team directly.<\/p>\n\n\n        <div id=\"expert_picks\">\n            <div class=\"header\">\n                                    <img decoding=\"async\" src=\"https:\/\/pabau.com\/wp-content\/uploads\/2025\/11\/Expert-Picks.svg\" alt=\"Continue your research\" height=\"42\" width=\"42\">\n                                <h3>Continue your research<\/h3>\n            <\/div>\n            <div class=\"content\">\n                                                            <div class=\"item\">\n                            <div>\n                                <svg width=\"20\" height=\"27\" viewBox=\"0 0 20 27\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\">\n                                    <path\n                                        d=\"M18.6223 14.3857C19.1246 13.8975 19.1246 13.1045 18.6223 12.6162L12.1938 6.36621C11.6915 5.87793 10.8759 5.87793 10.3737 6.36621C9.87143 6.85449 9.87143 7.64746 10.3737 8.13574L14.6125 12.2529H2.28571C1.57455 12.2529 1 12.8115 1 13.5029C1 14.1943 1.57455 14.7529 2.28571 14.7529H14.6085L10.3777 18.8701C9.87545 19.3584 9.87545 20.1514 10.3777 20.6396C10.8799 21.1279 11.6955 21.1279 12.1978 20.6396L18.6263 14.3896L18.6223 14.3857Z\"\n                                        fill=\"#54B2D3\" \/>\n                                <\/svg>\n                            <\/div>\n                            <p><strong>Need a structured approach to clinical note documentation?<\/strong> <a href=\"https:\/\/pabau.com\/guides\/safer-clinical-notes\/\" target=\"_blank\" rel=\"noopener\">Safer clinical notes<\/a> covers best practices for building defensible, audit-ready records across specialty settings.<\/p>\n                        <\/div>\n                                                                                <div class=\"item\">\n                            <div>\n                                <svg width=\"20\" height=\"27\" viewBox=\"0 0 20 27\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\">\n                                    <path\n                                        d=\"M18.6223 14.3857C19.1246 13.8975 19.1246 13.1045 18.6223 12.6162L12.1938 6.36621C11.6915 5.87793 10.8759 5.87793 10.3737 6.36621C9.87143 6.85449 9.87143 7.64746 10.3737 8.13574L14.6125 12.2529H2.28571C1.57455 12.2529 1 12.8115 1 13.5029C1 14.1943 1.57455 14.7529 2.28571 14.7529H14.6085L10.3777 18.8701C9.87545 19.3584 9.87545 20.1514 10.3777 20.6396C10.8799 21.1279 11.6955 21.1279 12.1978 20.6396L18.6263 14.3896L18.6223 14.3857Z\"\n                                        fill=\"#54B2D3\" \/>\n                                <\/svg>\n                            <\/div>\n                            <p><strong>Coding a different vascular diagnosis?<\/strong> ICD-10 code <a href=\"https:\/\/pabau.com\/diagnostic-codes\/icd-10-code-i81\/\" target=\"_blank\" rel=\"noopener\">I81<\/a> covers portal vein thrombosis documentation and billing.<\/p>\n                        <\/div>\n                                                                                <div class=\"item\">\n                            <div>\n                                <svg width=\"20\" height=\"27\" viewBox=\"0 0 20 27\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\">\n                                    <path\n                                        d=\"M18.6223 14.3857C19.1246 13.8975 19.1246 13.1045 18.6223 12.6162L12.1938 6.36621C11.6915 5.87793 10.8759 5.87793 10.3737 6.36621C9.87143 6.85449 9.87143 7.64746 10.3737 8.13574L14.6125 12.2529H2.28571C1.57455 12.2529 1 12.8115 1 13.5029C1 14.1943 1.57455 14.7529 2.28571 14.7529H14.6085L10.3777 18.8701C9.87545 19.3584 9.87545 20.1514 10.3777 20.6396C10.8799 21.1279 11.6955 21.1279 12.1978 20.6396L18.6263 14.3896L18.6223 14.3857Z\"\n                                        fill=\"#54B2D3\" \/>\n                                <\/svg>\n                            <\/div>\n                            <p><strong>Managing a patient with chronic disease-related wasting?<\/strong> ICD-10 code <a href=\"https:\/\/pabau.com\/diagnostic-codes\/icd-10-code-r64\/\" target=\"_blank\" rel=\"noopener\">R64<\/a> covers cachexia diagnosis and coding.<\/p>\n                        <\/div>\n                                                                                <div class=\"item\">\n                            <div>\n                                <svg width=\"20\" height=\"27\" viewBox=\"0 0 20 27\" fill=\"none\" xmlns=\"http:\/\/www.w3.org\/2000\/svg\">\n                                    <path\n                                        d=\"M18.6223 14.3857C19.1246 13.8975 19.1246 13.1045 18.6223 12.6162L12.1938 6.36621C11.6915 5.87793 10.8759 5.87793 10.3737 6.36621C9.87143 6.85449 9.87143 7.64746 10.3737 8.13574L14.6125 12.2529H2.28571C1.57455 12.2529 1 12.8115 1 13.5029C1 14.1943 1.57455 14.7529 2.28571 14.7529H14.6085L10.3777 18.8701C9.87545 19.3584 9.87545 20.1514 10.3777 20.6396C10.8799 21.1279 11.6955 21.1279 12.1978 20.6396L18.6263 14.3896L18.6223 14.3857Z\"\n                                        fill=\"#54B2D3\" \/>\n                                <\/svg>\n                            <\/div>\n                            <p><strong>Billing a home visit for a chronic disease follow-up?<\/strong> CPT code <a href=\"https:\/\/pabau.com\/procedure-codes\/cpt-code-99350\/\" target=\"_blank\" rel=\"noopener\">99350<\/a> covers established patient home visit billing.<\/p>\n                        <\/div>\n                                                <\/div>\n        <\/div>\n    \n\n\n<h2 id=\"h-frequently-asked-questions\" class=\"wp-block-heading\">Frequently asked questions<\/h2>\n\n\n\n<div class=\"schema-faq wp-block-yoast-faq-block\"><div class=\"schema-faq-section\" id=\"faq-question-1784274850104\"><h3 class=\"schema-faq-question\">What is ICD-10 Code M31.4 used for?<\/h3> <p class=\"schema-faq-answer\">ICD-10 Code M31.4 is the billable diagnosis code for aortic arch syndrome [Takayasu], used to document and bill for confirmed Takayasu arteritis. It is assigned when a clinician has confirmed a diagnosis of this large-vessel granulomatous vasculitis affecting the aorta and its main branches, and supports claim submission for associated rheumatology, vascular, and imaging procedures.<\/p> <\/div> <div class=\"schema-faq-section\" id=\"faq-question-1784274850105\"><h3 class=\"schema-faq-question\">Is M31.4 a billable ICD-10-CM code?<\/h3> <p class=\"schema-faq-answer\">Yes, M31.4 is a billable and specific ICD-10-CM code. No additional characters are required to make it valid for claim submission. It became effective October 1, 2025 for the 2026 ICD-10-CM edition and remains active.<\/p> <\/div> <div class=\"schema-faq-section\" id=\"faq-question-1784274850106\"><h3 class=\"schema-faq-question\">What is the ICD-9-CM equivalent of M31.4?<\/h3> <p class=\"schema-faq-answer\">The ICD-9-CM code that maps forward to M31.4 is 446.7 (Takayasu&#8217;s disease). This is an approximate, one-to-one forward mapping per the CMS General Equivalence Mappings (GEMs) file, making it one of the cleaner crosswalks in the vasculitis code group.<\/p> <\/div> <div class=\"schema-faq-section\" id=\"faq-question-1784274850107\"><h3 class=\"schema-faq-question\">What is the difference between M31.4 and other vasculitis codes like M31.5?<\/h3> <p class=\"schema-faq-answer\">M31.4 (Takayasu arteritis) and M31.5 (giant cell arteritis with polymyalgia rheumatica) are both large-vessel granulomatous vasculitides, but they differ by age of onset and vessel territory. M31.4 occurs under 40 years of age and affects the aorta and its main branches; M31.5 occurs over 50, has cranial artery involvement (temporal, ophthalmic), and co-occurs with polymyalgia rheumatica. Assign based on the confirmed diagnosis and documented clinical features, not the symptom presentation alone.<\/p> <\/div> <div class=\"schema-faq-section\" id=\"faq-question-1784274850108\"><h3 class=\"schema-faq-question\">What documentation is required to use ICD-10 Code M31.4?<\/h3> <p class=\"schema-faq-answer\">The medical record must contain a confirmed diagnosis statement (not &#8220;suspected&#8221; or &#8220;possible&#8221; for outpatient encounters), specialist attestation from a rheumatologist or vascular surgeon, named vessel involvement, disease activity status, and reference to imaging evidence such as CT angiography or MRI angiography findings demonstrating large-vessel stenosis or inflammation.<\/p> <\/div> <div class=\"schema-faq-section\" id=\"faq-question-1784274850109\"><h3 class=\"schema-faq-question\">Is aortic arch syndrome the same as Takayasu arteritis?<\/h3> <p class=\"schema-faq-answer\">Yes. Aortic arch syndrome is the ICD-10-CM label for the condition clinically known as Takayasu arteritis (also called Takayasu disease or pulseless disease). All three names are accepted in clinical documentation and map to the same code, M31.4, in the ICD-10-CM index.<\/p> <\/div> <\/div>\n","protected":false},"excerpt":{"rendered":"<p>ICD-10 Code M31.4 is the billable diagnosis code for aortic arch syndrome [Takayasu], the ICD-10-CM label for Takayasu arteritis. It covers confirmed cases of this large-vessel granulomatous vasculitis affecting the aorta and its main branches, effective October 1, 2025 for the 2026 ICD-10-CM edition. This reference covers ICD-10 Code M31.4 in full: its billable status, [&hellip;]<\/p>\n","protected":false},"author":77,"featured_media":157995,"comment_status":"closed","ping_status":"closed","sticky":false,"template":"","format":"standard","meta":{"_yoast_wpseo_linkdex":"91","_yoast_wpseo_content_score":"60","_yoast_wpseo_is_cornerstone":"","_yoast_wpseo_keywordsynonyms":"[\"\",\"\",\"\",\"\"]","_yoast_wpseo_focuskw_text_input":"","_seo_original_html":"","footnotes":""},"categories":[1549,1550],"tags":[4257,1386,4255,4256],"class_list":["post-157997","post","type-post","status-publish","format-standard","has-post-thumbnail","hentry","category-diagnostic-codes","category-icd-10-cm","tag-aortic-arch-syndrome-icd-10","tag-icd","tag-m31-4","tag-takayasu-arteritis-icd-10"],"yoast_head":"<!-- This site is optimized with the Yoast SEO Premium plugin v28.2 (Yoast SEO v28.2) - https:\/\/yoast.com\/product\/yoast-seo-premium-wordpress\/ -->\n<title>ICD-10 Code M31.4: Aortic arch syndrome 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is an all-in-one healthcare practice management software platform designed for clinics, medspas, therapists, and medical professionals. 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Outside of work, she's usually chasing her border collie around muddy fields or hunting down the best flat white in town.\",\"url\":\"https:\\\/\\\/pabau.com\\\/nl\\\/blog\\\/author\\\/katy-piper\\\/\"},{\"@type\":\"Question\",\"@id\":\"https:\\\/\\\/pabau.com\\\/nl\\\/diagnostic-codes\\\/icd-10-code-m314\\\/#faq-question-1784274850104\",\"position\":1,\"url\":\"https:\\\/\\\/pabau.com\\\/nl\\\/diagnostic-codes\\\/icd-10-code-m314\\\/#faq-question-1784274850104\",\"name\":\"What is ICD-10 Code M31.4 used for?\",\"answerCount\":1,\"acceptedAnswer\":{\"@type\":\"Answer\",\"text\":\"ICD-10 Code M31.4 is the billable diagnosis code for aortic arch syndrome [Takayasu], used to document and bill for confirmed Takayasu arteritis. It is assigned when a clinician has confirmed a diagnosis of this large-vessel granulomatous vasculitis affecting the aorta and its main branches, and supports claim submission for associated rheumatology, vascular, and imaging procedures.\",\"inLanguage\":\"nl-NL\"},\"inLanguage\":\"nl-NL\"},{\"@type\":\"Question\",\"@id\":\"https:\\\/\\\/pabau.com\\\/nl\\\/diagnostic-codes\\\/icd-10-code-m314\\\/#faq-question-1784274850105\",\"position\":2,\"url\":\"https:\\\/\\\/pabau.com\\\/nl\\\/diagnostic-codes\\\/icd-10-code-m314\\\/#faq-question-1784274850105\",\"name\":\"Is M31.4 a billable ICD-10-CM code?\",\"answerCount\":1,\"acceptedAnswer\":{\"@type\":\"Answer\",\"text\":\"Yes, M31.4 is a billable and specific ICD-10-CM code. No additional characters are required to make it valid for claim submission. 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This is an approximate, one-to-one forward mapping per the CMS General Equivalence Mappings (GEMs) file, making it one of the cleaner crosswalks in the vasculitis code group.\",\"inLanguage\":\"nl-NL\"},\"inLanguage\":\"nl-NL\"},{\"@type\":\"Question\",\"@id\":\"https:\\\/\\\/pabau.com\\\/nl\\\/diagnostic-codes\\\/icd-10-code-m314\\\/#faq-question-1784274850107\",\"position\":4,\"url\":\"https:\\\/\\\/pabau.com\\\/nl\\\/diagnostic-codes\\\/icd-10-code-m314\\\/#faq-question-1784274850107\",\"name\":\"What is the difference between M31.4 and other vasculitis codes like M31.5?\",\"answerCount\":1,\"acceptedAnswer\":{\"@type\":\"Answer\",\"text\":\"M31.4 (Takayasu arteritis) and M31.5 (giant cell arteritis with polymyalgia rheumatica) are both large-vessel granulomatous vasculitides, but they differ by age of onset and vessel territory. M31.4 occurs under 40 years of age and affects the aorta and its main branches; M31.5 occurs over 50, has cranial artery involvement (temporal, ophthalmic), and co-occurs with polymyalgia rheumatica. 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Aortic arch syndrome is the ICD-10-CM label for the condition clinically known as Takayasu arteritis (also called Takayasu disease or pulseless disease). 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Outside of work, she's usually chasing her border collie around muddy fields or hunting down the best flat white in town.","url":"https:\/\/pabau.com\/nl\/blog\/author\/katy-piper\/"},{"@type":"Question","@id":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/#faq-question-1784274850104","position":1,"url":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/#faq-question-1784274850104","name":"What is ICD-10 Code M31.4 used for?","answerCount":1,"acceptedAnswer":{"@type":"Answer","text":"ICD-10 Code M31.4 is the billable diagnosis code for aortic arch syndrome [Takayasu], used to document and bill for confirmed Takayasu arteritis. It is assigned when a clinician has confirmed a diagnosis of this large-vessel granulomatous vasculitis affecting the aorta and its main branches, and supports claim submission for associated rheumatology, vascular, and imaging procedures.","inLanguage":"nl-NL"},"inLanguage":"nl-NL"},{"@type":"Question","@id":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/#faq-question-1784274850105","position":2,"url":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/#faq-question-1784274850105","name":"Is M31.4 a billable ICD-10-CM code?","answerCount":1,"acceptedAnswer":{"@type":"Answer","text":"Yes, M31.4 is a billable and specific ICD-10-CM code. No additional characters are required to make it valid for claim submission. It became effective October 1, 2025 for the 2026 ICD-10-CM edition and remains active.","inLanguage":"nl-NL"},"inLanguage":"nl-NL"},{"@type":"Question","@id":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/#faq-question-1784274850106","position":3,"url":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/#faq-question-1784274850106","name":"What is the ICD-9-CM equivalent of M31.4?","answerCount":1,"acceptedAnswer":{"@type":"Answer","text":"The ICD-9-CM code that maps forward to M31.4 is 446.7 (Takayasu's disease). This is an approximate, one-to-one forward mapping per the CMS General Equivalence Mappings (GEMs) file, making it one of the cleaner crosswalks in the vasculitis code group.","inLanguage":"nl-NL"},"inLanguage":"nl-NL"},{"@type":"Question","@id":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/#faq-question-1784274850107","position":4,"url":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/#faq-question-1784274850107","name":"What is the difference between M31.4 and other vasculitis codes like M31.5?","answerCount":1,"acceptedAnswer":{"@type":"Answer","text":"M31.4 (Takayasu arteritis) and M31.5 (giant cell arteritis with polymyalgia rheumatica) are both large-vessel granulomatous vasculitides, but they differ by age of onset and vessel territory. M31.4 occurs under 40 years of age and affects the aorta and its main branches; M31.5 occurs over 50, has cranial artery involvement (temporal, ophthalmic), and co-occurs with polymyalgia rheumatica. Assign based on the confirmed diagnosis and documented clinical features, not the symptom presentation alone.","inLanguage":"nl-NL"},"inLanguage":"nl-NL"},{"@type":"Question","@id":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/#faq-question-1784274850108","position":5,"url":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/#faq-question-1784274850108","name":"What documentation is required to use ICD-10 Code M31.4?","answerCount":1,"acceptedAnswer":{"@type":"Answer","text":"The medical record must contain a confirmed diagnosis statement (not \"suspected\" or \"possible\" for outpatient encounters), specialist attestation from a rheumatologist or vascular surgeon, named vessel involvement, disease activity status, and reference to imaging evidence such as CT angiography or MRI angiography findings demonstrating large-vessel stenosis or inflammation.","inLanguage":"nl-NL"},"inLanguage":"nl-NL"},{"@type":"Question","@id":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/#faq-question-1784274850109","position":6,"url":"https:\/\/pabau.com\/nl\/diagnostic-codes\/icd-10-code-m314\/#faq-question-1784274850109","name":"Is aortic arch syndrome the same as Takayasu arteritis?","answerCount":1,"acceptedAnswer":{"@type":"Answer","text":"Yes. Aortic arch syndrome is the ICD-10-CM label for the condition clinically known as Takayasu arteritis (also called Takayasu disease or pulseless disease). All three names are accepted in clinical documentation and map to the same code, M31.4, in the ICD-10-CM index.","inLanguage":"nl-NL"},"inLanguage":"nl-NL"}]}},"yoast":{"focus_keyword":"ICD-10 Code M31.4","seo_title":"ICD-10 Code M31.4: Aortic arch syndrome [Takayasu]","meta_description":"Learn ICD-10 Code M31.4 for aortic arch syndrome (Takayasu arteritis): billable status, documentation rules, and related coding tips.","content_score":"60","is_cornerstone":"","related_keyphrases":[{"keyword":"vasculitis icd 10 code","score":67},{"keyword":"large vessel vasculitis icd 10","score":72},{"keyword":"pulseless disease icd 10 code","score":56}]},"_links":{"self":[{"href":"https:\/\/pabau.com\/nl\/wp-json\/wp\/v2\/posts\/157997","targetHints":{"allow":["GET"]}}],"collection":[{"href":"https:\/\/pabau.com\/nl\/wp-json\/wp\/v2\/posts"}],"about":[{"href":"https:\/\/pabau.com\/nl\/wp-json\/wp\/v2\/types\/post"}],"author":[{"embeddable":true,"href":"https:\/\/pabau.com\/nl\/wp-json\/wp\/v2\/users\/77"}],"replies":[{"embeddable":true,"href":"https:\/\/pabau.com\/nl\/wp-json\/wp\/v2\/comments?post=157997"}],"version-history":[{"count":4,"href":"https:\/\/pabau.com\/nl\/wp-json\/wp\/v2\/posts\/157997\/revisions"}],"predecessor-version":[{"id":182249,"href":"https:\/\/pabau.com\/nl\/wp-json\/wp\/v2\/posts\/157997\/revisions\/182249"}],"wp:featuredmedia":[{"embeddable":true,"href":"https:\/\/pabau.com\/nl\/wp-json\/wp\/v2\/media\/157995"}],"wp:attachment":[{"href":"https:\/\/pabau.com\/nl\/wp-json\/wp\/v2\/media?parent=157997"}],"wp:term":[{"taxonomy":"category","embeddable":true,"href":"https:\/\/pabau.com\/nl\/wp-json\/wp\/v2\/categories?post=157997"},{"taxonomy":"post_tag","embeddable":true,"href":"https:\/\/pabau.com\/nl\/wp-json\/wp\/v2\/tags?post=157997"}],"curies":[{"name":"wp","href":"https:\/\/api.w.org\/{rel}","templated":true}]}}